Reduced expression of ATP7B affected by Wilson disease-causing mutations is rescued by pharmacological folding chaperones 4-phenylbutyrate and curcumin.

P.V.E. van den Berghe; J.M. Stapelbroek; E. Krieger; P. de Bie; S.F.J. van de Graaf; R.E.A. de Groot; E.A.C.M. van Beurden; E. Spijker; R.H.J. Houwen; R. Berger; L.W.J. Klomp

Reduced expression of ATP7B affected by Wilson disease-causing mutations is rescued by pharmacological folding chaperones 4-phenylbutyrate and curcumin.

Translated title of the contribution: Reduced expression of ATP7B affected by Wilson disease-causing mutations is rescued by pharmacological folding chaperones 4-phenylbutyrate and curcumin.

P.V.E. van den Berghe
, J.M. Stapelbroek
, E. Krieger
, P. de Bie
, S.F.J. van de Graaf
, R.E.A. de Groot
, E.A.C.M. van Beurden
, E. Spijker
, R.H.J. Houwen
, R. Berger
, L.W.J. Klomp

Research output: Contribution to journal › Article › Academic › peer-review

Translated title of the contribution	Reduced expression of ATP7B affected by Wilson disease-causing mutations is rescued by pharmacological folding chaperones 4-phenylbutyrate and curcumin.
Original language	Undefined/Unknown
Pages (from-to)	1783-1795
Number of pages	13
Journal	Hepatology
Volume	50
Issue number	6
Publication status	Published - 2009

Keywords

Econometric and Statistical Methods: General
Geneeskunde(GENK)

Access to Document

http://www.ncbi.nlm.nih.gov/pubmed/19937698

Cite this

van den Berghe, P. V. E., Stapelbroek, J. M., Krieger, E., de Bie, P., van de Graaf, S. F. J., de Groot, R. E. A., van Beurden, E. A. C. M., Spijker, E., Houwen, R. H. J., Berger, R., & Klomp, L. W. J. (2009). Reduced expression of ATP7B affected by Wilson disease-causing mutations is rescued by pharmacological folding chaperones 4-phenylbutyrate and curcumin. Hepatology, 50(6), 1783-1795. http://www.ncbi.nlm.nih.gov/pubmed/19937698

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keywords = "Econometric and Statistical Methods: General, Geneeskunde(GENK)",

author = "\{van den Berghe\}, P.V.E. and J.M. Stapelbroek and E. Krieger and \{de Bie\}, P. and \{van de Graaf\}, S.F.J. and \{de Groot\}, R.E.A. and \{van Beurden\}, E.A.C.M. and E. Spijker and R.H.J. Houwen and R. Berger and L.W.J. Klomp",

year = "2009",

language = "Undefined/Unknown",

volume = "50",

pages = "1783--1795",

journal = "Hepatology",

issn = "0270-9139",

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van den Berghe, PVE, Stapelbroek, JM, Krieger, E, de Bie, P, van de Graaf, SFJ, de Groot, REA, van Beurden, EACM, Spijker, E, Houwen, RHJ, Berger, R & Klomp, LWJ 2009, 'Reduced expression of ATP7B affected by Wilson disease-causing mutations is rescued by pharmacological folding chaperones 4-phenylbutyrate and curcumin.', Hepatology, vol. 50, no. 6, pp. 1783-1795. <http://www.ncbi.nlm.nih.gov/pubmed/19937698>

TY - JOUR

T1 - Reduced expression of ATP7B affected by Wilson disease-causing mutations is rescued by pharmacological folding chaperones 4-phenylbutyrate and curcumin.

AU - van den Berghe, P.V.E.

AU - Stapelbroek, J.M.

AU - Krieger, E.

AU - de Bie, P.

AU - van de Graaf, S.F.J.

AU - de Groot, R.E.A.

AU - van Beurden, E.A.C.M.

AU - Spijker, E.

AU - Houwen, R.H.J.

AU - Berger, R.

AU - Klomp, L.W.J.

PY - 2009

Y1 - 2009

KW - Econometric and Statistical Methods: General

KW - Geneeskunde(GENK)

M3 - Article

SN - 0270-9139

VL - 50

SP - 1783

EP - 1795

JO - Hepatology

JF - Hepatology

IS - 6

ER -