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NAXCARE: a clinical outcome registry for Naxos disease and related cardiocutaneous syndromes

  • Adalena Tsatsopoulou*
  • , Dominic JR Abrams
  • , Aris Anastasakis
  • , Loizos Antoniades
  • , Elena Arbelo
  • , Eloisa Arbustini
  • , Euan A. Ashley
  • , Angeliki Asimaki
  • , Cristina Basso
  • , Eduardo Bossone
  • , Julia Cadrin-Turigny
  • , Hugh Calkins
  • , Andreina Carbone
  • , Perry M. Elliott
  • , Georgios Efthimiadis
  • , Monica Franzese
  • , Alexandra Frogoudaki
  • , Juan Ramon Gimeno
  • , John McGrath
  • , Jodie Ingles
  • Juan Pablo Kaski, Andre Keren, George Kohiadakis, Emilia Lazarou, George Lazaros, Stamatios Lerakis, Giuseppe Limongelli, Soultana Meditskou, Luisa Mestroni, Ioanna Metaxa, Emanuele Monda, Eustathios Papatheodorou, Despoina Parharidou, Alexandros Patrianakos, Kalliopi Pilichou, Alexandros Protonotarios, Ioannis Protonotarios, Salvatore Rega, Angelos Rigopoulos, Jeffrey Saffitz, Petros Syrris, Matt Taylor, Johannes Peter van Tintelen, Charalambos Vlachopoulos, Zafeirenia Xylouri, William J. McKenna
*Corresponding author for this work

Research output: Contribution to journalReview articlepeer-review

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Abstract

The NAXCARE (NAXos disease and Cardiocutaneous Assessment and Registry for Evaluation) is a global initiative designed to collect, store, and analyze clinical outcomes data on patients with Naxos disease and related cardiocutaneous syndromes (CCS). This registry aims to fill the gaps in clinical knowledge, enhance treatment approaches, and improve patient outcomes by systematically documenting disease progression, genetic profiles, and patient care pathways. The following methodology outlines the registry's design, data collection protocols, management, security measures, and anticipated contributions to research and clinical practice.

Original languageEnglish
Pages (from-to)147-159
Number of pages13
JournalHellenic Journal of Cardiology
Volume87
DOIs
Publication statusPublished - Jan 2026

Keywords

  • Arrhythmogenic right ventricular cardiomyopathy
  • Carvajal syndrome
  • Desmoplakin
  • Naxos disease
  • Palmoplantar keratoderma
  • Plakoglobin

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