TY - JOUR
T1 - Multifocale lymphangio-endotheliomatose met trombocytopenie (MLE-T)
T2 - vroegtijdige herkenning is van levensbelang
AU - Van Der Horst, M. N.
AU - Sillevis-Smitt, J.H.
AU - Peters, M. A.D.
AU - Middelkamp Hup, M. A.
AU - Van Den Berg, L.
AU - Wösten-Van Asperen, R.
AU - Kindermann, A.
AU - Merks, J. H.M.
PY - 2016/5/1
Y1 - 2016/5/1
N2 - Multifocal lymphangio-endotheliomatosis with thrombocytopenia (MLE-T) is an extremely rare disease and manifests itself with diffuse vascular cutaneous and gastrointestinal tract lesions, which can cause severe bleeding. The thrombocytopenia is chronic and fluctuating and thought to result from platelet trapping by the multifocal vascular lesions. We describe a newborn with numerous cutaneous and extracutaneous lesions who was successfully treated with thalidomide.
AB - Multifocal lymphangio-endotheliomatosis with thrombocytopenia (MLE-T) is an extremely rare disease and manifests itself with diffuse vascular cutaneous and gastrointestinal tract lesions, which can cause severe bleeding. The thrombocytopenia is chronic and fluctuating and thought to result from platelet trapping by the multifocal vascular lesions. We describe a newborn with numerous cutaneous and extracutaneous lesions who was successfully treated with thalidomide.
KW - Congenital vascular disease
KW - Diffuse neonatal hemangiomatosis
KW - MLE-T
KW - MLT
KW - Multifocal lymphangio-endotheliomatosis and thrombocytopenia
KW - Thalidomide
UR - http://www.scopus.com/inward/record.url?scp=85029509659&partnerID=8YFLogxK
M3 - Article
AN - SCOPUS:85029509659
SN - 0925-8604
VL - 26
SP - 314
EP - 317
JO - Nederlands Tijdschrift voor Dermatologie & Venereologie
JF - Nederlands Tijdschrift voor Dermatologie & Venereologie
IS - 5
ER -