Abstract
Meconium ileus (MI) is often the first manifestation of cystic fibrosis (CF) and occurs in approximately 20% of patients diagnosed with CF. This article reviews the pathophysiology of MI and its clinical presentation. It focuses on the medical and surgical management emphasizing the importance of nutrition and a multidisciplinary approach to improve both short-term and long-term outcomes for CF patients with MI.
Original language | English |
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Pages (from-to) | S32-S39 |
Journal | Journal of Cystic Fibrosis |
Volume | 16 |
Issue number | Suppl 2 |
DOIs | |
Publication status | Published - Nov 2017 |
Keywords
- Cystic fibrosis
- Gastrografin
- Meconium ileus
- Meconium peritonitis