Evaluation of left ventricular dimensions and function in Marfan's syndrome without significant valvular regurgitation

Lilian J Meijboom, Janneke Timmermans, Johan P van Tintelen, Gijs J Nollen, Julie De Backer, Maarten P van den Berg, Gerard H Boers, Barbara J M Mulder*

*Corresponding author for this work

Research output: Contribution to journalArticleAcademicpeer-review

Abstract

Left ventricular dimensions and systolic function were studied using echocardiography in 234 patients with Marfan's syndrome without significant valvular regurgitation. Left ventricular dimensions and systolic function were found to be normal in most patients with Marfan's syndrome. Some involvement of the left ventricle may have been present in a small group of these patients. No patients, however, fulfilled the criteria for dilated cardiomyopathy.

Original languageEnglish
Pages (from-to)795-797
Number of pages3
JournalThe American Journal of Cardiology
Volume95
Issue number6
DOIs
Publication statusPublished - 15 Mar 2005
Externally publishedYes

Keywords

  • Adolescent
  • Adrenergic beta-Antagonists/therapeutic use
  • Adult
  • Aged
  • Aortic Valve Insufficiency/diagnosis
  • Cardiac Volume/drug effects
  • Cardiomyopathy, Dilated/diagnosis
  • Echocardiography/drug effects
  • Female
  • Follow-Up Studies
  • Humans
  • Male
  • Marfan Syndrome/diagnosis
  • Middle Aged
  • Mitral Valve Insufficiency/diagnosis
  • Myocardial Contraction/drug effects
  • Ventricular Function, Left/drug effects

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