Abstract
A 12 year old boy suffering from p67-phox deficient chronic granulomatous disease presented with a bullous skin disease and a lung infection with paecilomyces species. The histopathology of a bullous lesion showed subepidermal blister formation and microabcesses containing eosinophils in the dermal papillae. By direct immunofluorescence, linear staining of IgA at the dermal-epidermal junction was detected which confirmed the clinical diagnosis of chronic bullous disease of childhood (linear IgA dermatosis).
| Original language | English |
|---|---|
| Pages (from-to) | 150-2 |
| Number of pages | 3 |
| Journal | Archives of Disease in Childhood |
| Volume | 77 |
| Issue number | 2 |
| Publication status | Published - Aug 1997 |
Keywords
- Amphotericin B
- Anti-Inflammatory Agents
- Antifungal Agents
- Autoimmune Diseases
- Child
- Drug Therapy, Combination
- Granulomatous Disease, Chronic
- Humans
- Itraconazole
- Lung Diseases, Fungal
- Male
- Paecilomyces
- Phosphoproteins
- Prednisolone
- Skin Diseases, Vesiculobullous
- Case Reports
- Journal Article
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